Giant cardiac tumours in the newborn: an unusual image

• Autorzy: Kwiatkowska J. , Ciemny S. , Kozlowski D.
• Języki publikacji: EN

Abstrakty

EN

Primary heart tumours in the paediatric population are very rare and they range from 0.01% to 0.04%. Most are benign lesions of which about half are rhabdomyomas. Rhabdomyoma tumour diagnosis is associated with a 75–80% risk of tuberous sclerosis complex (TSC). TSC are characterised with numerous changes of hamartoma-type located in the brain, kidneys, skin and other organs including the heart. More than two-thirds of newborns with TSC present rhabdomyomas in the heart. These changes may be asymptomatic, but in some cases they may cause heart failure, arrhythmias and death. We present a case report of an infant with giant rhabdomyoma tumours in the course of TSC. (Folia Morphol 2018; 77, 3: 601–603)

• Wydawca: -
• Czasopismo: Folia Morphologica
• Rocznik: 2018
• Tom: 77
• Numer: 3
• Opis fizyczny: p.601–603,fig.,ref.

Twórcy

autor

Kwiatkowska J.

• Department of Paediatric Cardiology and Congenital Heart Defects, Medical University of Gdansk, Debinki 7, 80–211 Gdansk, Poland

autor

Ciemny S.

• Department of Paediatric Cardiology and Congenital Heart Defects, Medical University of Gdansk, Debinki 7, 80–211 Gdansk, Poland

autor

Kozlowski D.

• Department of Cardiology and Electrotherapy, Medical University of Gdansk, Gdansk, Poland

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Identyfikatory

DOI

10.5603/FM.a2017.0119